Acquired thoracic dystrophy is a complication associated with early open repair of pectus excavatum resulting from extensive cartilage resection. The condition can cause serious functional and physiologic impairments, including cardiac compression and restrictive pulmonary function. We describe a 17-year-old boy with acquired thoracic dystrophy after Ravitch repair of pectus excavatum during infancy, whom we treated with distraction osteogenesis. The patient had a marked deformity of the chest wall and general hypoplasia of the central portion of the ribcage, with resultant symptomatic dyspnea on exertion and reduced pulmonary function. After osteotomies and distraction osteogenesis of bilateral ribs 4–8 using customized distraction devices, he had improved thoracic contour, resolution of dyspnea, and decreased restrictive pulmonary symptoms. This case suggests that distraction osteogenesis, already used extensively in craniomaxillofacial and orthopedic surgery, may be a novel method for management of this condition.
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March 2016
Case Report|
March 01 2016
Distraction Osteogenesis of Multiple Ribs for the Treatment of Acquired Thoracic Dystrophy
Merisa L. Piper, MD;
Merisa L. Piper, MD
Division of Plastic and Reconstructive Surgery, Department of Surgery, University of California, San Francisco, San Francisco, California
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Lawrence Delrosario, MD;
Lawrence Delrosario, MD
Division of Plastic and Reconstructive Surgery, Department of Surgery, University of California, San Francisco, San Francisco, California
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William Y. Hoffman, MD
Division of Plastic and Reconstructive Surgery, Department of Surgery, University of California, San Francisco, San Francisco, California
Address correspondence to William Hoffman, MD, Division of Plastic Surgery, University of California, San Francisco, 505 Parnassus Ave, Suite M593, San Francisco, CA 94143. E-mail: william.hoffman@ucsf.edu
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Address correspondence to William Hoffman, MD, Division of Plastic Surgery, University of California, San Francisco, 505 Parnassus Ave, Suite M593, San Francisco, CA 94143. E-mail: william.hoffman@ucsf.edu
POTENTIAL CONFLICT OF INTEREST: The authors have indicated they have no potential conflicts of interest to disclose.
FINANCIAL DISCLOSURE: The authors have indicated they have no financial relationships relevant to this article to disclose.
Pediatrics (2016) 137 (3): e20152053.
Article history
Accepted:
November 20 2015
Citation
Merisa L. Piper, Lawrence Delrosario, William Y. Hoffman; Distraction Osteogenesis of Multiple Ribs for the Treatment of Acquired Thoracic Dystrophy. Pediatrics March 2016; 137 (3): e20152053. 10.1542/peds.2015-2053
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