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TABLE 2

CCHD Lesions and Associated Clinical Characteristics

LesionPrevalenceaHypoxemiaDuctus Arteriosus Dependent
Outflow tract defects    
    Tetralogy of Fallot 6.1 Most Uncommon 
    D-transposition of the great arteries 4.0 All Uncommon 
    Double-outlet right ventricle 1.7 Some Some 
    Truncus arteriosus 1.0 All None 
TAPVC 1.2 All None 
Ebstein anomaly 0.6 Some Some 
Right obstructive defects    
    Tricuspid atresia 0.5 All Some 
    Pulmonary atresia, intact septum 0.8 All All 
    Pulmonic stenosis, atresia 6.3 Some Some 
Left obstructive defects    
    Hypoplastic left heart 3.3 All All 
    Coarctation of the aorta 4.7 Some Some 
    Aortic arch atresia or hypoplasia 1.0 Some All 
    Aortic valve stenosis (critical) 1.6 Uncommon Some 
Other major heart defects 12.4 Some Some 
LesionPrevalenceaHypoxemiaDuctus Arteriosus Dependent
Outflow tract defects    
    Tetralogy of Fallot 6.1 Most Uncommon 
    D-transposition of the great arteries 4.0 All Uncommon 
    Double-outlet right ventricle 1.7 Some Some 
    Truncus arteriosus 1.0 All None 
TAPVC 1.2 All None 
Ebstein anomaly 0.6 Some Some 
Right obstructive defects    
    Tricuspid atresia 0.5 All Some 
    Pulmonary atresia, intact septum 0.8 All All 
    Pulmonic stenosis, atresia 6.3 Some Some 
Left obstructive defects    
    Hypoplastic left heart 3.3 All All 
    Coarctation of the aorta 4.7 Some Some 
    Aortic arch atresia or hypoplasia 1.0 Some All 
    Aortic valve stenosis (critical) 1.6 Uncommon Some 
Other major heart defects 12.4 Some Some 

TAPVC indicates total anomalous pulmonary venous connection.

a

Per 10 000 livebirths. Data are derived from the Metropolitan Atlanta Congenital Defects Program.1

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